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Semin Neurol 2010; 30(4): 405-415
DOI: 10.1055/s-0030-1267284
© Thieme Medical Publishers

Unusual Peripheral Neuropathies. Part III: Intrinsic Inherited Causes

Matthew Grantz1
  • 1Department of Neurology, University of Utah, Salt Lake City, Utah
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Publication History

Publication Date:
12 October 2010 (online)

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ABSTRACT

Peripheral neuropathy is common and has many different etiologies. This is the last of three articles that review the less-common causes of peripheral neuropathy. Part III reviews the genetically coded causes of peripheral neuropathy, including those related to amyloidosis, neoplasm, paraproteinemias, as well as autosomal dominant, autosomal recessive, and x-linked causes. The extrinsic causes of neuropathy and the reactive or induced causes of neuropathy are covered in separate articles, Part I and Part II, respectively. The brief series reviews unusual causes of neuropathy and describes common presentations and the constellation of clinical findings. The goal is to help the clinician increase the diagnostic yield when sorting out the unusual causes of peripheral neuropathy.

KEYWORDS

Peripheral neuropathy - neuropathy - amyloidosis - paraneoplastic - paraproteinemia - inherited neuropathy

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Matthew GrantzM.D. 

Department of Neurology, University of Utah

175 North Medical Drive, Salt Lake City, UT 84132

Email: Matthew.Grantz@hsc.utah.edu

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