Early Surgical Management of Chylothorax Complicated by Gorham's Disease

Abstract

Gorham's disease is a rare disorder and its etiology remains unknown. It is characterized by the proliferation of vascular structures in bone, and results in progressive osteolysis. Chylothorax is a severe complication of Gorham's disease with a mortality of 50 %. We report a 14-year-old boy with Gorham's disease complicated by chylothorax who underwent early surgical management followed by radiotherapy.

Key words

Gorham's disease - chylothorax - thoracic duct ligation

References

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