Extramuraler GIST des Magens mit Manifestation durch Spontanruptur und akuter intraabdomineller Blutung mit Hämatoperitoneum

Zusammenfassung

Wir berichten über einen 38-jährigen Patienten mit einem großen extramural wachsenden gastrointestinalen Stromatumor (GIST) des Magens, der den gesamten linken Ober- und Mittelbauch einnahm und im Rahmen einer Spontanruptur mit konsekutivem Hämoperitoneum diagnostiziert wurde. Der Tumor konnte im Rahmen einer notfallmäßigen Laparotomie komplett entfernt werden. Aufgrund der Tumorruptur mit Serosadurchbruch und der histopathologischen Risikoeinschätzung als sog. high-risk GIST war eine adjuvante systemische Therapie indiziert. 

Abstract

We report on the case of a 38-year-old male patient with a huge extramural gastrointestinal stromal tumour (GIST) of the stomach, located in the left upper and middle abdominal cavity that was diagnosed on the basis of a spontaneous rupture and consecutive haemoperitoneum. The lesion was resected completely in an emergency operation. The tumour was classified as a high-risk lesion for aggressive biological behaviour and with regard to tumour rupture with perforation of the serosa, an adjuvant systemic therapy was indicated. 

Schlüsselwörter

abdomineller Notfalleingriff - Blutung - gastrointestinaler Stromatumor (GIST)

Key words

abdominal surgery - bleeding - gastrointestinal stromal tumour (GIST)

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