Abstract
Introduction
Atypical teratoid/rhabdoid tumors (AT/RT) are malignant central nervous system (CNS)
tumors that represent 3% of all pediatric CNS tumors. Majority of cases have SMARCB1
gene mutations and historically carried a poor prognosis.
Case Presentation
A 9-year-old boy was diagnosed with a third ventricle AT/RT and initially underwent
endoscopic surgical biopsy. Subsequent tumor resection was completed using an interhemispheric–transcortical
approach.
Lessons
Surgical approaches to ventricular system must be tailored to the tumor characteristics
on a case-by-case basis. We present a case using a transcortical approach for understanding
of the microsurgical anatomy for safe resection of a third ventricle AT/RT.
Keywords
AT/RT - atypical teratoid/rhabdoid tumor - ventricular surgery - pediatric neuro-oncology
- high-grade glioma
