Linksventrikuläre Non-Compaction-Kardiomyopathie

Die linksventrikuläre Non-Compaction-Kardiomyopathie ist eine genetische Erkrankung des Myokards, die durch eine auffällige Hypertrabekularisierung gekennzeichnet ist. Im Einzelfall ist die Abgrenzung zur Hypertrabekularisierung bei anderen Herzerkrankungen schwierig. Dieser Beitrag gibt einen Überblick über die multimodale Diagnostik einschließlich Echokardiografie, kardialer Magnetresonanztomografie sowie Genetik, die zur Diagnosestellung beitragen kann.

Schlüsselwörter

Kardiomyopathie - Hypertrabekularisierung - Genetik - Echokardiografie - Therapie

• Literatur

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