CC BY-NC-ND 4.0 · Endosc Int Open 2019; 07(09): E1163-E1165
DOI: 10.1055/a-0977-2614
Case report
Owner and Copyright © Georg Thieme Verlag KG 2019

Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland

Leonardo Blas Jhon
Endoscopy Department, University Hospital Fundacion Jimenez Diaz, Madrid, Spain
,
Paloma Sánchez-Fayos
Endoscopy Department, University Hospital Fundacion Jimenez Diaz, Madrid, Spain
,
Maria Jesus Martín Relloso
Endoscopy Department, University Hospital Fundacion Jimenez Diaz, Madrid, Spain
,
Daniel Calero Barón
Endoscopy Department, University Hospital Fundacion Jimenez Diaz, Madrid, Spain
,
Juan Carlos Porres Cubero
Endoscopy Department, University Hospital Fundacion Jimenez Diaz, Madrid, Spain
› Author Affiliations
Further Information

Publication History

submitted 10 October 2018

accepted after revision 21 June 2019

Publication Date:
29 August 2019 (online)

Abstract

Primitive neuroectodermal tumors (PNET) are very rare tumors that belong to a family of malignant neoplasms of tiny round cells which are derived from the neural crest. This report discusses a rare case of an adult woman with esophageal PNET, confirmed by immunohistochemistry, that presented with metastasis to the pineal gland. To our knowledge, this is the first case report of a PNET with these features. Despite surgery and chemotherapeutic treatment, our case has shown disease progression.