Aortic regurgitation in Behçet's disease with aortitis and myxoid degeneration of the aortic valve leaflets

Abstract

A case of Behçet's disease (BD) associated with aortic regurgitation (AR) is presented. The patient had all four major criteria of BD. He also had AR complicated by pulmonary edema and heart failure. He was medically treated for his hemodynamic status after which he had an aortic valve replacement operation. The histopathological examination of the aortic wall revealed lymphocytic vasculitis of vasovasorum and fibrous thickening, and myxoid degeneration was observed in the aortic leaflets.