Ewing's Sarcoma of Frontal Bone: A Rare Case

Abstract

Primary Ewing's sarcoma arising from frontal bone is rare. We report a case of 17-year-old boy with painless swelling in the frontoparietal region. Computed tomography showed destruction of bone and an enhancing extradural mass. The patient underwent wide excision combined with radio and chemotherapy. Histopathology revealed it to be round cell sarcoma, and immunohistochemistry confirmed it to be Ewing's sarcoma.

Keywords

primary Ewing's sarcoma - round cell tumor - frontoparietal bone

• References

• 1 Tsokos M. Peripheral primitive neuroectodermal tumors. Diagnosis, classification, and prognosis. Perspect Pediatr Pathol 1992; 16: 27-98
• 2 Steinbok P, Flodmark O, Norman MG, Chan KW, Fryer CJ. Primary Ewing's sarcoma of the base of the skull. Neurosurgery 1986; 19 (01) 104-107
• 3 Angervall L, Enzinger FM. Extraskeletal neoplasm resembling Ewing's sarcoma. Cancer 1975; 36 (01) 240-251
• 4 Jaffe R, Santamaria M, Yunis EJ. et al. The neuroectodermal tumor of bone. Am J Surg Pathol 1984; 8 (12) 885-898
• 5 Singh P, Jain M, Singh DP, Kalra N, Khandelwal N, Suri S. MR findings of primary Ewing's sarcoma of greater wing of sphenoid. Australas Radiol 2002; 46 (04) 409-411
• 6 Srihari K, Bindu PM, Ramreddy KV, Moorthy RS, Reddy GR. A rare case of atypical primary Ewing's sarcoma of occipital bone. J Evid Based Med Healthcare 2016; 3 (56) 2934-2936
• 7 Mishra HB, Haran RP, Joseph T, Chandi SM. Primary Ewing's sarcoma of the skull. A report of two cases. Br. J Neurosurg 1993; 7 (06) 683-686 (Case Rep)
• 8 Kuzeyli K, Aktürk F, Reis A. et al. Primary Ewing's sarcoma of the temporal bone with intracranial, extracranial and intraorbital extension. Case report. Neurosurg Rev 1997; 20 (02) 132-134
• 9 Erol FS, Ozveren MF, Ozercan IH, Topsakal C, Akdemir I. Primary Ewing's sarcoma of the occipital bone—case report. Neurol Med Chir (Tokyo) 2001; 41 (04) 206-209